|
|
Lifespan’s A - Z Health Information Library |
||||||||||
Incontinentia pigmenti achromiansDefinitionIncontinentia pigmenti achromians is a rare birth defect that causes unusual patches of light-colored (hypopigmented) skin and possible neurological and skeletal problems. See also: Hypopigmentation Alternative NamesHypomelanosis of Ito (more commonly used) CausesThe cause is unknown. It is slightly more common in girls than in boys. Symptoms
Exams and TestsA Wood's lamp examination of the skin lesions may help confirm the diagnosis. Your doctor may also recommend chromosome analysis or a further medical workup to discover any related medical problems. TreatmentThere is no treatment for the hypopigmentation. Treatment consists of treating the symptoms. Cosmetics or clothing may be used to cover the hypopigmented spots if desired. Seizures, scoliosis, and other problems are treated as necessary. Outlook (Prognosis)What happens depends on the type and severity of symptoms that develop. In most cases, the skin pigment eventually returns to normal. Possible Complications
When to Contact a Medical ProfessionalCall your health care provider if your child exhibits an unusual pattern of the color of the skin. ReferencesGenodermatoses and Congenital Anomolies. In: James WD, Berger TG, Elston DM, eds. Andrews' Diseases of the Skin: Clinical Dermatology. 10th ed. Philadelphia, Pa: Saunders Elsevier; 2005: chap 27. Moss C. Mosaicism and Linear Lesions. In: Bolognia JL, Jorizzo JL, Rapini RP, eds.: Dermatology. 2nd ed. Philadelphia, Pa: Mosby Elsevier; 2008: chap 61. Review Date: 8/26/2009
Reviewed By: Kevin Berman, MD, PhD, Atlanta Center for Dermatologic Disease, Atlanta, GA. Review provided by VeriMed Healthcare Network; Linda Vorvick, MD, Medical Director, MEDEX Northwest Division of Physician Assistant Studies, University of Washington School of Medicine. Also reviewed by David Zieve, MD, MHA, Medical Director, A.D.A.M., Inc. The information provided herein should not be used during any
medical emergency or for the diagnosis or treatment of any medical
condition. A licensed medical professional should be consulted for
diagnosis and treatment of any and all medical conditions. Call 911
for all medical emergencies. Links to other sites are provided for
information only -- they do not constitute endorsements of those
other sites. © 1997- A.D.A.M., Inc. Any duplication or distribution of the
information contained herein is strictly prohibited.
 |
||||||||||
|
|
